Juvenile dermatomyositis.
نویسنده
چکیده
Juvenile dermatomyositis (JDMS) is a chronic inflammatory condition characterized by muscle weakness and a distinctive rash caused by underlying vasculopathy. Long-term complications include subcutaneous and muscular calcification, contractures and in some cases the gradual development of a second connective tissue disease. Early aggressive treatment with systemic immunosuppressants and other agents such as intravenous immunoglobulin (IVIG) reduces mortality and morbidity.
منابع مشابه
Non-Hodgkin lymphoma in a 13-year-old boy with provisional hypomyopathic juvenile Dermatomyositis
Provisional hypomyopathic juvenile dermatomyositis is a subgroup of clinically amyopathic juvenile dermatomyositis provisional. The diagnostic criteria include: Classic dermatomyositis skin lesions – which have to be confirmed by biopsy –, no involvement of proximal muscles, subclinical involvement of these muscles and normal level of muscle enzymes. These criteria should be present for a minim...
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INTRODUCTION Infections can act as a trigger for juvenile dermatomyositis, with a predominance of respiratory tract infections reported previously. We present the first case of juvenile dermatomyositis following varicella infection to be described in the literature. CASE PRESENTATION A 15-month-old Caucasian girl was diagnosed with juvenile dermatomyositis 3 months after a varicella infection...
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A link between dermatomyositis and neoplasia has long been suspected. The precise incidence of this association remains controversial, owing to varying criteria used to diagnose dermatomyositis. Although juvenile dermatomyositis is believed to display no association with neoplasm, there have been few reported cases of dermatomyositis associated with tumors of any kind in pediatric age group (1-...
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Dermatomyositis is a well-known autoimmune disorder. On the other hand, juvenile amyopathic dermatomyositis (JADM) occurs rather rarely. Here, we report an unusual case in a 9-year-old Turkish boy showing a unilateral linear inflammatory skin lesion that was followed, after 16 months, by the appearance of bilateral disseminated features JADM.
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ورودعنوان ژورنال:
- Reumatizam
دوره 48 1 شماره
صفحات -
تاریخ انتشار 1989